B-ENT

Pneumosinus dilatans and orbital meningioma in neurofibromatosis type 2

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Department of Otolaryngology-Head and Neck Surgery

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Department of Ophthalmology

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Department of Pathology, University Hospitals Leuven, Belgium

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Center of Human Genetics University Hospital Gasthuisberg, KULeuven, Herestraat 49, 3000 Leuven, Belgium

B-ENT 2005; 1: 89-92
Read: 813 Downloads: 571 Published: 22 February 2020

Pneumosinus dilatans and orbital meningioma in neurofibromatosis type 2. We report on a 9-year-old boy with neurofibromatosis type 2 and a progressive proptosis of the left eye. Imaging studies revealed a pneumosinus dilatans of the left ethmoidal and frontal sinuses and an adjacent left orbital mass. Incision biopsy of the orbital mass showed a meningiothelial meningioma. Orbital and intracranial meningiomas are frequently associated with pneumosinus dilatans. This report illustrates the relationship of pneumosinus dilatans, intra-orbital meningioma and neurofibromatosis type 2.

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EISSN 2684-4907